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Dernières publications
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
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Ingo Riederer, Daniella Arêas Mendes-Da-Cruz, Guilherme Cordenonsi da Fonseca, Mariela Natacha González, Otavio Brustolini, et al.. Zika virus disrupts gene expression in human myoblasts and myotubes: Relationship with susceptibility to infection. PLoS Neglected Tropical Diseases, 2022, 16 (2), pp.e0010166. ⟨10.1371/journal.pntd.0010166⟩. ⟨hal-03832616⟩
Chiffres clés
98
Publications avec texte intégral
Open Access
59 %
Mots clés
Arbovirus
Alzheimer's disease
Muscle stem cells
Aged
Autoimmune diseases
PABPN1
Gene replacement
Exon-skipping
Muscle strength
Fibrosis
Aav-U7
Neuromuscular junction NMJ
Skeletal muscle
Ageing
Oculopharyngeal muscular dystrophy
Transcriptomics
Myotube
FAPs
Differentiation
Sarcopenia
Botulinum neurotoxin
ARN
Anti-fibrotic pharmacotherapies
Myoblast
GENE
Calcium
Dystrophin
AAV vectors
Gene therapy
Duchenne muscular dystrophy
ALS
Agrégats de PABPN1
Bioinformatics
PABPN1 agregates
Myoblasts
Biopsies humaines
Triplet expansion disease
Xenograft
Adipose tissue
DMD
Pax7
Myopathy
Satellite cell
Myopathies
C2 domains
Aggregate
2-D PAGE
AAV
Autologous
Myosin
Intercellular communication
CS
Biomarker
Accelerometry
Dystrophie musculaire oculopharyngée
Akt
Thérapie génique
Actin
Muscle fibrosis
Inflammation
BINDING SPECIFICITY
Myositis
Satellite cells
AChR antibodies
Pharyngeal muscle
Haploinsufficiency
Geriatric assessment
CNOT6L
Alphavirus
OPMD
DUX4
C2C12 cells
CD49d
Cell therapy
Bioinformatique
Metabolism
Annexin A2
MUTATIONS
APOPTOSIS
Human
Dysferlin
Andermann syndrome
DNA methylation
RNA
Myogenesis
AUTOPHAGY
Muscle dystrophy
Antiserum
Cross-bridge kinetics
Antisens oligonucleotides
Anti-acetylcholine receptor antibodies
FSHD
Atrophy
Regeneration
Dysferlinopathy
Lamins
Muscle
Functional genomics
Bile salt hydrolases
Nuclear envelope